Gene Uniprot Gene Full Name Protein Class pLI DSI g DPI g Num. diseases
SDHB P21912 succinate dehydrogenase complex iron sulfur subunit B Enzyme 2.4E-04 0.474 0.846 10
SDHD O14521 succinate dehydrogenase complex subunit D Transporter 0.34 0.472 0.885 9
SDHAF2 Q9NX18 succinate dehydrogenase complex assembly factor 2 2.8E-06 0.604 0.692 7
BCS1L Q9Y276 BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone 4.7E-13 0.534 0.808 6
SDHC Q99643 succinate dehydrogenase complex subunit C 2.0E-04 0.517 0.846 6
NDUFS3 O75489 NADH:ubiquinone oxidoreductase core subunit S3 5.8E-04 0.581 0.769 5
NDUFS8 O00217 NADH:ubiquinone oxidoreductase core subunit S8 Enzyme 0.17 0.636 0.538 5
COX15 Q7KZN9 cytochrome c oxidase assembly homolog COX15 1.1E-13 0.638 0.538 4
FOXRED1 Q96CU9 FAD dependent oxidoreductase domain containing 1 Enzyme 2.0E-16 0.633 0.462 4
NDUFS1 P28331 NADH:ubiquinone oxidoreductase core subunit S1 Enzyme 6.6E-11 0.595 0.692 4
NDUFS2 O75306 NADH:ubiquinone oxidoreductase core subunit S2 Enzyme 1.4E-03 0.601 0.654 4
NDUFS7 O75251 NADH:ubiquinone oxidoreductase core subunit S7 0.91 0.579 0.769 4
SURF1 Q15526 SURF1 cytochrome c oxidase assembly factor Enzyme 1.6E-13 0.578 0.654 4
TACO1 Q9BSH4 translational activator of cytochrome c oxidase I 1.5E-03 0.647 0.577 4
TTC19 Q6DKK2 tetratricopeptide repeat domain 19 1.4E-08 0.663 0.385 4
COX10 Q12887 cytochrome c oxidase assembly factor heme A:farnesyltransferase COX10 Enzyme 8.4E-02 0.623 0.654 3
FASTKD2 Q9NYY8 FAST kinase domains 2 2.9E-06 0.659 0.731 3
NDUFA1 O15239 NADH:ubiquinone oxidoreductase subunit A1 0.55 0.636 0.423 3
NDUFA10 O95299 NADH:ubiquinone oxidoreductase subunit A10 Enzyme 6.2E-08 0.678 0.385 3
NDUFA11 Q86Y39 NADH:ubiquinone oxidoreductase subunit A11 1.8E-02 0.705 0.308 3
NDUFA13 Q9P0J0 NADH:ubiquinone oxidoreductase subunit A13 Enzyme 3.8E-06 0.556 0.692 3
NDUFA2 O43678 NADH:ubiquinone oxidoreductase subunit A2 Enzyme 0.77 0.617 0.577 3
NDUFAF1 Q9Y375 NADH:ubiquinone oxidoreductase complex assembly factor 1 3.6E-03 0.700 0.308 3
NDUFAF3 Q9BU61 NADH:ubiquinone oxidoreductase complex assembly factor 3 5.3E-03 0.650 0.577 3