Entrez Id: |
4338 |
Gene Symbol: |
MOCS2 |
MOCS2
|
O96007 O96033
|
molybdenum cofactor synthesis 2
|
|
39
|
0.729 |
0.308 |
4.6E-04 |
0.200 |
None
|
|
0
|
0
|
|
|
Entrez Id: |
249 |
Gene Symbol: |
ALPL |
ALPL
|
P05186
|
alkaline phosphatase, biomineralization associated
|
Enzyme
|
190
|
0.546 |
0.769 |
3.6E-04 |
0.080 |
None
|
1.000 |
8
|
0
|
2000 |
2019 |
Entrez Id: |
5053 |
Gene Symbol: |
PAH |
PAH
|
P00439
|
phenylalanine hydroxylase
|
|
219
|
0.516 |
0.769 |
6.4E-23 |
0.080 |
None
|
1.000 |
8
|
0
|
1995 |
2019 |
Entrez Id: |
875 |
Gene Symbol: |
CBS |
CBS
|
P0DN79 P35520
|
cystathionine beta-synthase
|
Enzyme
|
295
|
0.465 |
0.885 |
3.1E-05 |
0.060 |
None
|
1.000 |
6
|
2
|
2001 |
2019 |
Entrez Id: |
412 |
Gene Symbol: |
STS |
STS
|
P08842
|
steroid sulfatase
|
Enzyme
|
382
|
0.431 |
0.846 |
0.81 |
0.040 |
None
|
1.000 |
4
|
0
|
1989 |
2002 |
Entrez Id: |
102724560 |
Gene Symbol: |
CBSL |
CBSL
|
P0DN79 P35520
|
cystathionine beta-synthase like
|
|
129
|
0.540 |
0.808 |
|
0.040 |
None
|
1.000 |
4
|
0
|
2001 |
2019 |
Entrez Id: |
95 |
Gene Symbol: |
ACY1 |
ACY1
|
Q03154
|
aminoacylase 1
|
|
62
|
0.653 |
0.577 |
6.9E-09 |
0.030 |
None
|
1.000 |
3
|
0
|
2005 |
2014 |
Entrez Id: |
3081 |
Gene Symbol: |
HGD |
HGD
|
Q93099
|
homogentisate 1,2-dioxygenase
|
Enzyme
|
70
|
0.631 |
0.577 |
3.0E-08 |
0.030 |
None
|
1.000 |
3
|
0
|
2008 |
2017 |
Entrez Id: |
2639 |
Gene Symbol: |
GCDH |
GCDH
|
Q92947
|
glutaryl-CoA dehydrogenase
|
|
72
|
0.691 |
0.385 |
4.9E-03 |
0.030 |
None
|
1.000 |
3
|
0
|
2000 |
2019 |
Entrez Id: |
2717 |
Gene Symbol: |
GLA |
GLA
|
P06280
|
galactosidase alpha
|
|
190
|
0.537 |
0.769 |
1.00 |
0.030 |
None
|
1.000 |
3
|
0
|
1997 |
2007 |
Entrez Id: |
1892 |
Gene Symbol: |
ECHS1 |
ECHS1
|
P30084
|
enoyl-CoA hydratase, short chain 1
|
Enzyme
|
93
|
0.601 |
0.654 |
8.8E-04 |
0.030 |
None
|
1.000 |
3
|
0
|
2014 |
2018 |
Entrez Id: |
3704 |
Gene Symbol: |
ITPA |
ITPA
|
Q9BY32
|
inosine triphosphatase
|
Enzyme
|
77
|
0.604 |
0.500 |
1.0E-07 |
0.310 |
None
|
1.000 |
3
|
0
|
2002 |
2019 |
Entrez Id: |
34 |
Gene Symbol: |
ACADM |
ACADM
|
P11310
|
acyl-CoA dehydrogenase medium chain
|
Enzyme
|
94
|
0.638 |
0.462 |
2.1E-12 |
0.030 |
None
|
1.000 |
3
|
0
|
1993 |
2016 |
Entrez Id: |
4594 |
Gene Symbol: |
MMUT |
MMUT
|
P22033
|
methylmalonyl-CoA mutase
|
Enzyme
|
147
|
0.534 |
0.731 |
1.7E-22 |
0.320 |
None
|
1.000 |
3
|
0
|
2009 |
2018 |
Entrez Id: |
5009 |
Gene Symbol: |
OTC |
OTC
|
P00480
|
ornithine carbamoyltransferase
|
|
135
|
0.565 |
0.846 |
0.87 |
0.030 |
None
|
1.000 |
3
|
0
|
1985 |
2009 |
Entrez Id: |
1593 |
Gene Symbol: |
CYP27A1 |
CYP27A1
|
Q02318
|
cytochrome P450 family 27 subfamily A member 1
|
Enzyme
|
167
|
0.538 |
0.731 |
5.3E-19 |
0.030 |
None
|
1.000 |
3
|
0
|
1992 |
2018 |
Entrez Id: |
2592 |
Gene Symbol: |
GALT |
GALT
|
P07902
|
galactose-1-phosphate uridylyltransferase
|
Enzyme
|
87
|
0.612 |
0.654 |
2.1E-06 |
0.030 |
None
|
1.000 |
3
|
0
|
1998 |
2017 |
Entrez Id: |
29958 |
Gene Symbol: |
DMGDH |
DMGDH
|
Q9UI17
|
dimethylglycine dehydrogenase
|
Enzyme
|
15
|
0.890 |
0.154 |
2.1E-24 |
0.020 |
None
|
1.000 |
2
|
0
|
1999 |
2001 |
Entrez Id: |
3251 |
Gene Symbol: |
HPRT1 |
HPRT1
|
P00492
|
hypoxanthine phosphoribosyltransferase 1
|
Enzyme
|
210
|
0.500 |
0.808 |
0.94 |
0.020 |
None
|
1.000 |
2
|
0
|
2008 |
2010 |
Entrez Id: |
38 |
Gene Symbol: |
ACAT1 |
ACAT1
|
P24752
|
acetyl-CoA acetyltransferase 1
|
Enzyme
|
176
|
0.538 |
0.692 |
9.9E-08 |
0.020 |
None
|
1.000 |
2
|
0
|
2004 |
2010 |
Entrez Id: |
3145 |
Gene Symbol: |
HMBS |
HMBS
|
P08397
|
hydroxymethylbilane synthase
|
Enzyme
|
140
|
0.559 |
0.731 |
0.95 |
0.020 |
None
|
1.000 |
2
|
0
|
1994 |
1995 |
Entrez Id: |
7167 |
Gene Symbol: |
TPI1 |
TPI1
|
P60174
|
triosephosphate isomerase 1
|
Enzyme
|
184
|
0.517 |
0.846 |
3.0E-02 |
0.300 |
None
|
1.000 |
2
|
0
|
1986 |
1993 |
Entrez Id: |
6232 |
Gene Symbol: |
RPS27 |
RPS27
|
P42677
|
ribosomal protein S27
|
Nucleic acid binding
|
104
|
0.578 |
0.769 |
0.76 |
0.020 |
None
|
1.000 |
2
|
0
|
2019 |
2019 |
Entrez Id: |
3425 |
Gene Symbol: |
IDUA |
IDUA
|
P35475
|
alpha-L-iduronidase
|
Enzyme
|
258
|
0.499 |
0.846 |
3.8E-13 |
0.020 |
None
|
1.000 |
2
|
0
|
2019 |
2019 |
Entrez Id: |
2582 |
Gene Symbol: |
GALE |
GALE
|
Q14376
|
UDP-galactose-4-epimerase
|
|
30
|
0.722 |
0.385 |
1.5E-10 |
0.020 |
None
|
1.000 |
2
|
0
|
1995 |
1998 |