Entrez Id: |
26275 |
Gene Symbol: |
HIBCH |
HIBCH
|
Q6NVY1
|
3-hydroxyisobutyryl-CoA hydrolase
|
Enzyme
|
60
|
0.700 |
0.500 |
2.6E-13 |
0.010 |
None
|
1.000 |
1
|
0
|
2014 |
2014 |
Entrez Id: |
38 |
Gene Symbol: |
ACAT1 |
ACAT1
|
P24752
|
acetyl-CoA acetyltransferase 1
|
Enzyme
|
176
|
0.538 |
0.692 |
9.9E-08 |
0.020 |
None
|
1.000 |
2
|
0
|
2004 |
2010 |
Entrez Id: |
34 |
Gene Symbol: |
ACADM |
ACADM
|
P11310
|
acyl-CoA dehydrogenase medium chain
|
Enzyme
|
94
|
0.638 |
0.462 |
2.1E-12 |
0.030 |
None
|
1.000 |
3
|
0
|
1993 |
2016 |
Entrez Id: |
197322 |
Gene Symbol: |
ACSF3 |
ACSF3
|
Q4G176
|
acyl-CoA synthetase family member 3
|
Enzyme
|
35
|
0.743 |
0.308 |
2.3E-26 |
0.010 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
ADAMTSL2
|
Q86TH1
|
ADAMTS like 2
|
Enzyme
|
61
|
0.666 |
0.346 |
1.6E-03 |
0.300 |
None
|
1.000 |
1
|
0
|
2008 |
2008 |
Entrez Id: |
158 |
Gene Symbol: |
ADSL |
ADSL
|
P30566
|
adenylosuccinate lyase
|
Enzyme
|
84
|
0.631 |
0.654 |
8.9E-12 |
0.020 |
None
|
1.000 |
2
|
0
|
2011 |
2013 |
Entrez Id: |
64902 |
Gene Symbol: |
AGXT2 |
AGXT2
|
Q9BYV1
|
alanine--glyoxylate aminotransferase 2
|
|
25
|
0.729 |
0.385 |
3.7E-28 |
0.300 |
None
|
1.000 |
1
|
0
|
2011 |
2011 |
Entrez Id: |
189 |
Gene Symbol: |
AGXT |
AGXT
|
P21549
|
alanine--glyoxylate and serine--pyruvate aminotransferase
|
Enzyme
|
94
|
0.593 |
0.731 |
1.2E-07 |
0.010 |
None
|
1.000 |
1
|
0
|
2003 |
2003 |
Entrez Id: |
440138 |
Gene Symbol: |
ALG11 |
ALG11
|
Q2TAA5
|
ALG11 alpha-1,2-mannosyltransferase
|
|
47
|
0.722 |
0.346 |
6.2E-09 |
0.010 |
None
|
1.000 |
1
|
0
|
2019 |
2019 |
Entrez Id: |
249 |
Gene Symbol: |
ALPL |
ALPL
|
P05186
|
alkaline phosphatase, biomineralization associated
|
Enzyme
|
190
|
0.546 |
0.769 |
3.6E-04 |
0.080 |
None
|
1.000 |
8
|
0
|
2000 |
2019 |
Entrez Id: |
3425 |
Gene Symbol: |
IDUA |
IDUA
|
P35475
|
alpha-L-iduronidase
|
Enzyme
|
258
|
0.499 |
0.846 |
3.8E-13 |
0.020 |
None
|
1.000 |
2
|
0
|
2019 |
2019 |
Entrez Id: |
95 |
Gene Symbol: |
ACY1 |
ACY1
|
Q03154
|
aminoacylase 1
|
|
62
|
0.653 |
0.577 |
6.9E-09 |
0.030 |
None
|
1.000 |
3
|
0
|
2005 |
2014 |
Entrez Id: |
383 |
Gene Symbol: |
ARG1 |
ARG1
|
P05089
|
arginase 1
|
Enzyme
|
273
|
0.476 |
0.846 |
3.6E-04 |
0.010 |
None
|
1.000 |
1
|
0
|
2014 |
2014 |
Entrez Id: |
445 |
Gene Symbol: |
ASS1 |
ASS1
|
P00966
|
argininosuccinate synthase 1
|
Enzyme
|
163
|
0.523 |
0.731 |
1.5E-09 |
0.020 |
None
|
1.000 |
2
|
0
|
1983 |
2001 |
Entrez Id: |
440 |
Gene Symbol: |
ASNS |
ASNS
|
P08243
|
asparagine synthetase (glutamine-hydrolyzing)
|
Enzyme
|
90
|
0.595 |
0.692 |
9.4E-06 |
0.010 |
None
|
1.000 |
1
|
0
|
2018 |
2018 |
Entrez Id: |
443 |
Gene Symbol: |
ASPA |
ASPA
|
P45381
|
aspartoacylase
|
|
123
|
0.564 |
0.731 |
4.1E-04 |
0.010 |
None
|
1.000 |
1
|
0
|
2012 |
2012 |
Entrez Id: |
5826 |
Gene Symbol: |
ABCD4 |
ABCD4
|
O14678
|
ATP binding cassette subfamily D member 4
|
Transporter
|
26
|
0.769 |
0.308 |
1.3E-12 |
0.300 |
None
|
1.000 |
1
|
0
|
2012 |
2012 |
Entrez Id: |
540 |
Gene Symbol: |
ATP7B |
ATP7B
|
P35670
|
ATPase copper transporting beta
|
Transporter
|
182
|
0.529 |
0.654 |
4.8E-30 |
0.010 |
None
|
1.000 |
1
|
0
|
2013 |
2013 |
Entrez Id: |
760 |
Gene Symbol: |
CA2 |
CA2
|
P00918
|
carbonic anhydrase 2
|
|
210
|
0.506 |
0.808 |
1.7E-06 |
0.020 |
None
|
1.000 |
2
|
0
|
1985 |
1986 |
Entrez Id: |
1066 |
Gene Symbol: |
CES1 |
CES1
|
P23141
|
carboxylesterase 1
|
Enzyme
|
80
|
0.590 |
0.692 |
3.3E-15 |
0.300 |
None
|
1.000 |
1
|
0
|
2008 |
2008 |
Entrez Id: |
1120 |
Gene Symbol: |
CHKB |
CHKB
|
Q9Y259
|
choline kinase beta
|
Kinase
|
48
|
0.663 |
0.423 |
3.8E-07 |
0.010 |
None
|
1.000 |
1
|
0
|
2016 |
2016 |
Entrez Id: |
57017 |
Gene Symbol: |
COQ9 |
COQ9
|
O75208
|
coenzyme Q9
|
|
41
|
0.700 |
0.423 |
5.5E-06 |
0.010 |
None
|
1.000 |
1
|
0
|
2020 |
2020 |
Entrez Id: |
875 |
Gene Symbol: |
CBS |
CBS
|
P0DN79 P35520
|
cystathionine beta-synthase
|
Enzyme
|
295
|
0.465 |
0.885 |
3.1E-05 |
0.060 |
None
|
1.000 |
6
|
2
|
2001 |
2019 |
Entrez Id: |
102724560 |
Gene Symbol: |
CBSL |
CBSL
|
P0DN79 P35520
|
cystathionine beta-synthase like
|
|
129
|
0.540 |
0.808 |
|
0.040 |
None
|
1.000 |
4
|
0
|
2001 |
2019 |
Entrez Id: |
1593 |
Gene Symbol: |
CYP27A1 |
CYP27A1
|
Q02318
|
cytochrome P450 family 27 subfamily A member 1
|
Enzyme
|
167
|
0.538 |
0.731 |
5.3E-19 |
0.030 |
None
|
1.000 |
3
|
0
|
1992 |
2018 |