No significant correlation was observed between rs504348 genotypes and CF disease severity, but pancreatic insufficient CF subjects showed increased colonization with any form of <i>Pseudomonas aeruginosa</i> (OR = 3.125, 95% CI: 1.192-8.190) and mucoid <i>P. aeruginosa</i> (OR = 5.075, 95% CI: 1.307-28.620) compared to the pancreatic sufficient group.