Sensorineural Hearing Loss (disorder)
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
783
|
111
|
0.130 |
None |
0.667 |
3 |
1
|
2002 |
2011 |
Usher syndrome type 2
|
disease |
Pathological Conditions, Signs and Symptoms; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Eye Diseases; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
8
|
16
|
0.320 |
None |
1.000 |
3 |
|
2005 |
2016 |
Low Vision
|
disease |
Pathological Conditions, Signs and Symptoms; Eye Diseases; Nervous System Diseases
|
Disease or Syndrome
|
157
|
51
|
0.020 |
None |
1.000 |
2 |
|
1999 |
2017 |
Low frequency deafness
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
15
|
1
|
0.020 |
None |
1.000 |
2 |
|
2002 |
2011 |
Leber Congenital Amaurosis
|
disease |
Eye Diseases
|
Disease or Syndrome
|
83
|
109
|
0.020 |
None |
1.000 |
2 |
|
2011 |
2014 |
Usher Syndrome, Type III
|
disease |
Pathological Conditions, Signs and Symptoms; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Eye Diseases; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
13
|
24
|
0.310 |
None |
1.000 |
2 |
|
1996 |
2005 |
Usher Syndrome, Type II
|
disease |
Pathological Conditions, Signs and Symptoms; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Eye Diseases; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
12
|
7
|
0.500 |
None |
1.000 |
2 |
|
2005 |
2014 |
Auditory neuropathy spectrum disorder
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
28
|
17
|
0.020 |
None |
1.000 |
2 |
|
2002 |
2017 |
Macular Edema, Cystoid
|
disease |
Eye Diseases
|
Disease or Syndrome
|
49
|
3
|
0.010 |
None |
1.000 |
1 |
|
2019 |
2019 |
Retinal Diseases
|
group |
Eye Diseases
|
Disease or Syndrome
|
714
|
56
|
0.010 |
None |
1.000 |
1 |
|
2010 |
2010 |
Endolymphatic Hydrops
|
disease |
Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
11
|
1
|
0.010 |
None |
< 0.001 |
1 |
|
2011 |
2011 |
Age related macular degeneration
|
disease |
Eye Diseases
|
Disease or Syndrome
|
685
|
663
|
0.010 |
None |
1.000 |
1 |
|
2013 |
2013 |
Blindness, Legal
|
disease |
Pathological Conditions, Signs and Symptoms; Eye Diseases; Nervous System Diseases
|
Disease or Syndrome
|
10
|
|
0.010 |
None |
1.000 |
1 |
|
2017 |
2017 |
Recessive sensorineural hearing loss
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
4
|
1
|
0.010 |
None |
1.000 |
1 |
|
2016 |
2016 |
Sensorineural hearing loss, bilateral
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
117
|
30
|
0.300 |
None |
1.000 |
1 |
|
2012 |
2012 |
Bardet-Biedl Syndrome
|
disease |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Eye Diseases; Nervous System Diseases
|
Disease or Syndrome
|
86
|
163
|
0.010 |
None |
1.000 |
1 |
|
1999 |
1999 |
Inherited hearing loss
|
disease |
|
Disease or Syndrome
|
13
|
|
0.010 |
None |
1.000 |
1 |
|
2011 |
2011 |
Deafness, Autosomal Dominant 12
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
2
|
20
|
0.010 |
None |
1.000 |
1 |
|
1997 |
1997 |
Deafness, Autosomal Dominant 9
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
4
|
10
|
0.010 |
None |
1.000 |
1 |
|
2002 |
2002 |
Progressive sensorineural hearing impairment
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
78
|
28
|
0.110 |
None |
1.000 |
1 |
1
|
2008 |
2008 |
Profound sensorineural hearing loss
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
22
|
4
|
0.010 |
None |
1.000 |
1 |
|
2017 |
2017 |
Auditory neuropathy
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
24
|
20
|
0.010 |
None |
1.000 |
1 |
|
2002 |
2002 |
STARGARDT DISEASE 1 (disorder)
|
disease |
|
Disease or Syndrome
|
23
|
317
|
0.010 |
None |
1.000 |
1 |
|
2014 |
2014 |
Deafness, Autosomal Dominant 13
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
6
|
3
|
0.010 |
None |
1.000 |
1 |
|
2002 |
2002 |
Deaf-Blind Disorders
|
group |
Pathological Conditions, Signs and Symptoms; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Eye Diseases; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
11
|
2
|
0.010 |
None |
1.000 |
1 |
|
2011 |
2011 |