Gene Uniprot Gene Full Name Protein Class pLI DSI g DPI g Num. diseases
ATPAF2 Q8N5M1 ATP synthase mitochondrial F1 complex assembly factor 2 2.2E-09 0.729 0.423 2
BCS1L Q9Y276 BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone 4.7E-13 0.534 0.808 6
COX10 Q12887 cytochrome c oxidase assembly factor heme A:farnesyltransferase COX10 Enzyme 8.4E-02 0.623 0.654 3
COX15 Q7KZN9 cytochrome c oxidase assembly homolog COX15 1.1E-13 0.638 0.538 4
COX4I1 P13073 cytochrome c oxidase subunit 4I1 0.39 0.691 0.500 1
COX4I2 Q96KJ9 cytochrome c oxidase subunit 4I2 1.4E-04 0.716 0.500 2
COX6B1 P14854 cytochrome c oxidase subunit 6B1 0.12 0.700 0.577 2
FASTKD2 Q9NYY8 FAST kinase domains 2 2.9E-06 0.659 0.731 3
FOXRED1 Q96CU9 FAD dependent oxidoreductase domain containing 1 Enzyme 2.0E-16 0.633 0.462 4
LRPPRC P42704 leucine rich pentatricopeptide repeat containing 2.3E-10 0.493 0.769 2
NDUFA1 O15239 NADH:ubiquinone oxidoreductase subunit A1 0.55 0.636 0.423 3
NDUFA10 O95299 NADH:ubiquinone oxidoreductase subunit A10 Enzyme 6.2E-08 0.678 0.385 3
NDUFA11 Q86Y39 NADH:ubiquinone oxidoreductase subunit A11 1.8E-02 0.705 0.308 3
NDUFA13 Q9P0J0 NADH:ubiquinone oxidoreductase subunit A13 Enzyme 3.8E-06 0.556 0.692 3
NDUFA2 O43678 NADH:ubiquinone oxidoreductase subunit A2 Enzyme 0.77 0.617 0.577 3
NDUFA8 P51970 NADH:ubiquinone oxidoreductase subunit A8 Enzyme 0.34 1.000 0.077 1
NDUFAF1 Q9Y375 NADH:ubiquinone oxidoreductase complex assembly factor 1 3.6E-03 0.700 0.308 3
NDUFAF3 Q9BU61 NADH:ubiquinone oxidoreductase complex assembly factor 3 5.3E-03 0.650 0.577 3
NDUFAF4 Q9P032 NADH:ubiquinone oxidoreductase complex assembly factor 4 0.55 0.686 0.385 3
NDUFAF5 Q5TEU4 NADH:ubiquinone oxidoreductase complex assembly factor 5 3.1E-10 0.674 0.462 3
NDUFS1 P28331 NADH:ubiquinone oxidoreductase core subunit S1 Enzyme 6.6E-11 0.595 0.692 4
NDUFS2 O75306 NADH:ubiquinone oxidoreductase core subunit S2 Enzyme 1.4E-03 0.601 0.654 4
NDUFS3 O75489 NADH:ubiquinone oxidoreductase core subunit S3 5.8E-04 0.581 0.769 5
NDUFS4 O43181 NADH:ubiquinone oxidoreductase subunit S4 3.1E-04 0.587 0.808 3