Vohwinkel Syndrome, Variant Form
|
disease |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
4
|
|
0.550 |
None |
1.000 |
7 |
|
1998 |
2010 |
Squamous cell carcinoma
|
disease |
Neoplasms
|
Neoplastic Process
|
2507
|
257
|
0.310 |
None |
1.000 |
2 |
|
2006 |
2008 |
Erythrokeratodermia variabilis
|
disease |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
13
|
8
|
0.310 |
None |
1.000 |
1 |
|
2014 |
2014 |
Skin Neoplasms
|
group |
Neoplasms; Skin and Connective Tissue Diseases
|
Neoplastic Process
|
363
|
9
|
0.300 |
None |
1.000 |
1 |
|
2008 |
2008 |
Malignant neoplasm of skin
|
disease |
Neoplasms; Skin and Connective Tissue Diseases
|
Neoplastic Process
|
508
|
38
|
0.300 |
None |
1.000 |
1 |
|
2008 |
2008 |
Congenital Nonbullous Ichthyosiform Erythroderma
|
disease |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
36
|
16
|
0.110 |
None |
1.000 |
1 |
|
2001 |
2001 |
Keratoderma, Palmoplantar
|
disease |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
165
|
19
|
0.110 |
None |
1.000 |
1 |
|
2001 |
2001 |
Erythema
|
phenotype |
Pathological Conditions, Signs and Symptoms; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
227
|
8
|
0.100 |
None |
|
0 |
|
|
|
Cutaneous plaque
|
phenotype |
|
Finding
|
19
|
107
|
0.100 |
None |
|
0 |
|
|
|
Parakeratosis
|
disease |
Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
31
|
|
0.100 |
None |
|
0 |
|
|
|
Onychogryposis
|
disease |
Pathological Conditions, Signs and Symptoms; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
17
|
|
0.100 |
None |
|
0 |
|
|
|
Hyperkeratosis
|
disease |
Pathological Conditions, Signs and Symptoms; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
176
|
19
|
0.100 |
None |
|
0 |
|
|
|
Hypergranulosis
|
phenotype |
|
Finding
|
16
|
|
0.100 |
None |
|
0 |
|
|
|
Honeycomb palmoplantar keratoderma
|
phenotype |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases
|
Finding
|
3
|
|
0.100 |
None |
|
0 |
|
|
|
Hyperkeratosis, CTCAE
|
phenotype |
|
Finding
|
87
|
|
0.100 |
None |
|
0 |
|
|
|
Dystrophia unguium
|
disease |
Pathological Conditions, Signs and Symptoms; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
81
|
9
|
0.100 |
None |
|
0 |
|
|
|
Sensorineural Hearing Loss (disorder)
|
disease |
Pathological Conditions, Signs and Symptoms; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Disease or Syndrome
|
783
|
111
|
0.100 |
None |
|
0 |
|
|
|
Orthokeratosis
|
phenotype |
Skin and Connective Tissue Diseases
|
Finding
|
10
|
|
0.100 |
None |
|
0 |
|
|
|
Amniotic Bands
|
disease |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
|
Congenital Abnormality
|
6
|
|
0.100 |
None |
|
0 |
|
|
|
Mutilating keratoderma
|
disease |
Pathological Conditions, Signs and Symptoms; Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases; Musculoskeletal Diseases; Nervous System Diseases; Otorhinolaryngologic Diseases
|
Congenital Abnormality
|
9
|
24
|
0.060 |
None |
1.000 |
6 |
|
1998 |
2019 |
Psoriasis
|
disease |
Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
1308
|
705
|
0.030 |
None |
0.667 |
3 |
|
2004 |
2009 |
Dermatologic disorders
|
group |
Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
617
|
21
|
0.020 |
None |
1.000 |
2 |
|
2000 |
2010 |
Dermatitis, Atopic
|
disease |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases; Immune System Diseases
|
Disease or Syndrome
|
751
|
232
|
0.020 |
None |
1.000 |
2 |
|
2006 |
2008 |
Adult T-Cell Lymphoma/Leukemia
|
disease |
Neoplasms; Immune System Diseases; Hemic and Lymphatic Diseases
|
Neoplastic Process
|
540
|
11
|
0.020 |
None |
1.000 |
2 |
|
1985 |
1987 |
Ichthyosiform Erythroderma, Congenital
|
disease |
Congenital, Hereditary, and Neonatal Diseases and Abnormalities; Skin and Connective Tissue Diseases
|
Disease or Syndrome
|
31
|
11
|
0.010 |
None |
1.000 |
1 |
|
2001 |
2001 |